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sarcome d'ewing

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Ewing's sarcoma is a highly aggressive malignant tumor that primarily affects bone and soft tissue, most frequently occurring in children and adolescents
9
Abstract

9.

Ewing sarcoma

PubMed
Highly cited
. It is the second most common bone tumor in this age group
.

Pathology and diagnosis

Clinical presentation

Management

Prognosis

  • The prognosis for Ewing's sarcoma varies. The survival rate is 70–80% for patients with standard-risk and localized disease but drops to approximately 30% for those with metastatic disease

In conclusion, Ewing's sarcoma is a highly aggressive malignant tumor primarily affecting bone and soft tissue in children and adolescents. It is characterized by specific genetic translocations and small round cells expressing CD99. Management involves a combination of surgery, radiotherapy, and chemotherapy, with prognosis varying based on the extent of the disease at diagnosis.

References

1

Ewing's sarcoma

Medical management

Guidelines

Management of advanced/metastatic disease

Pathway
ERN/.../ERN GENTURIS/ERN