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ACR/EULAR classification criteria for eosinophilic granulomatosis with polyangiitis

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When to use
Evidence of small- or medium-vessel vasculitis on imaging
No
Yes
Alternative diagnoses mimicking vasculitis are excluded
No
Yes
Obstructive airway disease
No
Yes
Nasal polyps
No
Yes
Mononeuritis multiplex
No
Yes
Blood eosinophil count ≥ 1×10**9/L
No
Yes
Extravascular eosinophilic-predominant inflammation on biopsy
No
Yes
Positive test for cytoplasmic antineutrophil cytoplasmic antibodies or anti-proteinase 3 antibodies
No
Yes
Hematuria
No
Yes
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